Table 1 Current classification of the SSc [66]

Pachydermia of the hands, proximal metacarpophalangeal joint (adequate criterion)

9

Pachydermia of the fingers

(only the highest points)

Swelling of the fingers (puffy fingers)

Sclerodactyly

2

4

Lesions to the fingertips

(only the highest points)

Ulcers of the fingertips

Scars on the fingertips (pitting scars)

2

3

Teleangiectasias

2

Abnormal peryonchial capillaries

2

Pulmonary participation

(max. 2 points)

Pulmonary arterial hypertension

Interstitial lung disease

2

2

Raynaud´s phenomenon

3

SSc-typical autoantibodies

(max. 3 points)

Anti-centromere

Anti-Topoisomerase I (Scl70)

Anti-RNA Polymerase III

3